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KMID : 0371320100790010075
Journal of the Korean Surgical Society
2010 Volume.79 No. 1 p.75 ~ p.78
Heterotaxia Syndrome with Intraluminal Duodenal Diverticulum
Kim Jae-Hun

Song Geun-Am
Kim Suk
Seo Hyung-Il
Kim Hyun-Sung
Kim Dae-Hwan
Jeon Tae-Yong
Abstract
Both heterotaxia and intraluminal duodenal diverticulum (IDD) are uncommon congenital anomalies. Heterotaxia is a group of situs anomalies and IDD is a type of duodenal atresia. Heterotaxia is commonly associated with intraabdominal abnormalities causing intestinal obstruction, but heterotaxia with IDD is extremely rare. Herein we report a case of 21-year-old female who presented with symptoms of duodenal obstruction due to IDD associated with heterotaxia. This is the second
KEYWORD
Heterotaxia, Situs ambiguous, Polysplenia, Intraluminal duodenal diverticulum, Virtual endoscopy
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